Isfahan University of Medical Sciences Journal of Isfahan Medical School 1027-7595 26 89 2008 06 21 The Phakomatosis (Neurocutaneous Syndromes): Sturge-Weber Syndrome The Phakomatosis (Neurocutaneous Syndromes): Sturge-Weber Syndrome 214 12972 FA Ahmad Chitsaz Associate Professor, Faculty of Neurology, School of Medicine, Isfahan University of Medical Sciences 0000-0001-7983-2122 Journal Article 2010 11 07   Neurocutaneous syndromes or phakomatosis are inherited or sporadic conditions that feature lesions of both skin and nervous system. Sturge-weber syndrome (SWS) is characterized by a facial cutaneaous angioma (port-wine nevus) and an associated leptomeningeal and brain angioma; Neurological features of SWS are mental retardation, contra lateral hemiparesis and hemiatrophy and homonymous hemianopia.   Sturge-Weber Syndrome (SWS)   Neurocutaneous syndromes or phakomatosis are inherited or sporadic conditions that feature lesions of both skin and nervous system. Sturge-weber syndrome (SWS) is characterized by a facial cutaneaous angioma (port-wine nevus) and an associated leptomeningeal and brain angioma; Neurological features of SWS are mental retardation, contra lateral hemiparesis and hemiatrophy and homonymous hemianopia.   Sturge-Weber Syndrome (SWS)