A Rare Case of Lymphangiomyomatosis with Bilateral Pneumothorax: Di-agnosis and Treatment

Document Type : Case Report

Authors

1 Assistant Professor, Department of Surgery, School of Medicine, Lorestan University of Medical Sciences, Khorramabad, Iran

2 Assistant Professor, Department of Internal Medicine, School of Medicine, Lorestan University of Medical Sciences, Khorramabad, Iran

3 Assistant Professor, Department of Pathology, School of Medicine, Lorestan University of Medical Sciences, Khorramabad, Iran

4 Researcher, Lorestan University of Medical Sciences, Khorramabad, Iran

Abstract

Background: lymphangioleiomyomatosisis (LAM) a rare and progressive lung disease in young women that can lead to death due to respiratory failure. LAM affects women in childbearing age. Respiratory distress, pneumothorax and chylothorax are the manifestation of this disease.Case report: The patient was a 42-year-old woman with relapsing pneumathorax and several boluses in both lungs. She underwent the 2-stage bilateral thoracotomy. She had no complications in a 15-months follow-up period.

Keywords

References

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Journal of Isfahan Medical School
Volume 29, Issue 147 - Serial Number 147
May and June 2011
Pages 947-951

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History

  • Receive Date: 16 March 2011
  • Revise Date: 01 November 2024
  • Accept Date: 06 April 2022

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